Overview of Pulmonary Hypertension in Systemic Scleroderma
3.4 هزار بار بازدید -
13 سال پیش
-
Pulmonary hypertension is not the
Pulmonary hypertension is not the same as "regular" high blood pressure or hypertension which can be easily measured with a blood pressure test.
Pulmonary hypertension is a high pressure in the arteries between the heart and lungs or pulmonary arteries and is a type of vascular disease that can be found in people with scleroderma.
There are dozens of causes of pulmonary hypertension, ranging from genetics, medications or street drugs, connective tissue diseases such as scleroderma, heart and lung diseases, and blood disorders.
Primary Pulmonary Hypertension occurs by itself and not secondary to another illness, such as scleroderma. When pulmonary hypertension occurs along with other lung, heart, or systemic connective tissue disease such as scleroderma it is called Secondary Pulmonary Hypertension. The distinction is important because treatments and their effectiveness can vary depending upon whether the pulmonary hypertension is primary or secondary.
Although Doppler ECHO can suggest pulmonary hypertension it cannot be definitely diagnosed without right heart catheterization.
Initially there may be no symptoms at all then later symptoms can include shortness of breath, weakness, and fatigue with exertion. As it progresses people become very tired after only slight activity. Eventually they experience right-sided heart failure and death. However the course of mild to moderate pulmonary hypertension in scleroderma is still unknown and it's possible that it may remain unchanged for long periods of time.
Early diagnosis and treatment substantially improves the prognosis for pulmonary hypertension secondary to systemic scleroderma which is why it is essential to be treated by a recognised scleroderma expert.
Presented by. Amanda Thorpe on behalf of the nonprofit International Scleroderma Network at sclero.org.
Pulmonary hypertension is a high pressure in the arteries between the heart and lungs or pulmonary arteries and is a type of vascular disease that can be found in people with scleroderma.
There are dozens of causes of pulmonary hypertension, ranging from genetics, medications or street drugs, connective tissue diseases such as scleroderma, heart and lung diseases, and blood disorders.
Primary Pulmonary Hypertension occurs by itself and not secondary to another illness, such as scleroderma. When pulmonary hypertension occurs along with other lung, heart, or systemic connective tissue disease such as scleroderma it is called Secondary Pulmonary Hypertension. The distinction is important because treatments and their effectiveness can vary depending upon whether the pulmonary hypertension is primary or secondary.
Although Doppler ECHO can suggest pulmonary hypertension it cannot be definitely diagnosed without right heart catheterization.
Initially there may be no symptoms at all then later symptoms can include shortness of breath, weakness, and fatigue with exertion. As it progresses people become very tired after only slight activity. Eventually they experience right-sided heart failure and death. However the course of mild to moderate pulmonary hypertension in scleroderma is still unknown and it's possible that it may remain unchanged for long periods of time.
Early diagnosis and treatment substantially improves the prognosis for pulmonary hypertension secondary to systemic scleroderma which is why it is essential to be treated by a recognised scleroderma expert.
Presented by. Amanda Thorpe on behalf of the nonprofit International Scleroderma Network at sclero.org.
13 سال پیش
در تاریخ 1390/09/08 منتشر شده
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